George Shaker Igbayilola Dosunmu Jason Kim Tiffany Guillen Kevin Kuang
HCA Healthcare
01-01-2023
Please see supplemental content for full abstract. Short QT syndrome (SQTS) is a rare inherited arrhythmogenic disorder characterized by abnormally short QT interval on electrocardiogram (ECG) seconda..
Please see supplemental content for full abstract. Short QT syndrome (SQTS) is a rare inherited arrhythmogenic disorder characterized by abnormally short QT interval on electrocardiogram (ECG) secondary to a cardiac channelopathy in the absence of structural heart disease.3 Defective function of the potassium-calcium ion channels in SQTS patients facilitates an increased risk of ventricular and atrial arrhythmias, which can lead to symptoms such as syncope or cardiac arrest.2 In this report, we present a 24-year-old male with a past medical history SQTS with prior cardiac arrest and ventricular fibrillation, status post ICD placement and cardiac sympathectomy, who presented with increased palpitations and ICD firing. Additionally, we discuss the epidemiology, pathophysiology, presentation, diagnostic criteria, prognosis, and treatment of SQTS.
