Acute Plasma Cell Leukemia Presenting as Primary Hyperammonemic Encephalopathy

Authors

Dveet Patel, HCA HealthcareFollow
Andrew Mangano, HCA HealthcareFollow
David Moccia, HCA HealthcareFollow
Shawn Esperti, HCA HealthcareFollow
Kunjan Udani, HCA HealthcareFollow
Jordan Henderson
Nino Balanchivadze, Henry Ford Health SystemFollow

Division

South Atlantic

Hospital

Grand Strand Medical Center

Document Type

Case Report

Publication Date

10-2020

Keywords

Plasma cell leukemia, Hyperammonemic encephalopathy, Multiple myeloma

Disciplines

Hematology | Hemic and Lymphatic Diseases | Neoplasms | Oncology

Abstract

Primary plasma cell leukemia (PPCL) is a rare form of multiple myeloma (MM) and is a rare aggressive disease with a median overall survival of 6 - 11 months. We present a case of acute hyperammonemic encephalopathy as the initial presentation of PPCL in a 78-year-old woman to highlight an atypical presentation of this disorder.

Publisher or Conference

Journal of Medical Cases

Recommended Citation

Patel D, Mangano A, Moccia D, et al. Acute Plasma Cell Leukemia Presenting as Primary Hyperammonemic Encephalopathy. J Med Cases. 2020;11(10):320-323. https://doi.org/10.14740/jmc3559